Oral and craniofacial manifestations of Ellis-Van Creveld syndrome: a systematic review

Authors

  • D Lauritano Department of medicine and surgery, Neuroscience Centre of Milan, University of Milan-Bicocca, Milan
  • S Attuati Department of medicine and surgery, Neuroscience Centre of Milan, University of Milan-Bicocca, Milan
  • M Besana Department of medicine and surgery, Neuroscience Centre of Milan, University of Milan-Bicocca, Milan
  • G Rodilosso Department of medicine and surgery, Neuroscience Centre of Milan, University of Milan-Bicocca, Milan
  • V Quinzi Post Graduate School of Orthodontics, Department of Life, Health and Environmental Sciences, University of L'Aquila
  • G Marzo Post Graduate School of Orthodontics, Department of Life, Health and Environmental Sciences, University of L'Aquila
  • F Carinci Department of Morphology, Surgery and Experimental Medicine, University of Ferrara, Ferrara

DOI:

https://doi.org/10.23804/ejpd.2019.20.04.09

Keywords:

Ellis-Van Creveld syndrome, chondroectodermal dysplasia, dental anomalies, malocclusion, rare diseases

Abstract

AIM: A systematic literature review on oral and craniofacial manifestations of Ellis-Van Creveld syndrome was performed. METHODS: From 2 databases were selected 74 articles using as key words "Ellis-Van Creveld" AND "Oral" OR "Craniofacial" OR "Dental" OR "Malocclusion". Prisma protocol was used to create an eligible list for the screening. Data were collected in a table to compare the clinical aspects found. CONCLUSION: Through this analysis oral and cranio-facial manifestations of Ellis-Van Creveld syndrome were pointed out. Management of Ellis-Van Creveld syndrome requires a multidisciplinary approach involving different clinicians; dentists play an important role in early diagnosis and treatment of the patients.