Otodental Syndrome

Authors

  • M Paglia Department of Paediatric Dentistry, Istituto Stomatologico Italiano, Milano
  • M Severino Researcher Department of Medicine and Surgery University of Perugia, Perugia
  • R Gatto Ordinary Professor in Paediatric Dentistry, Department of Life, Health and Enviromental Science, Paediatric Dentistry, University of L'Aquila, L'Aquila
  • G Giani Private Practice in Busto Arsizio, Varese
  • S Caruso Department of Life, Health and Enviromental Science, Paediatric Dentistry, University of L'Aquila, L'Aquila

DOI:

https://doi.org/10.23804/ejpd.2023.24.03.03

Keywords:

Otodental syndrome, globodontia, sensorineural hearing loss

Abstract

BACKGROUND: Otodental syndrome is a rare autosomal dominant condition characterised by a dental phenotype known as globodontia often associated with high-frequency hearing loss. Globodontia occurs both in the decidous and permanent dentition and affects canine and molar teeth.